Fibrosi retroperitoneale idiopatica: descrizione di due casi

Idiopathic Retroperitoneal Fibrosis (IRF) is a rare syndrome of unknown origin, possibly of autoimmune nature, which leads to the compression and obstruction of ureteres and other adjacent organs. We describe two paediatric cases of IRF which represent the wide spectrum of clinical expression and evolution of this disease. The diagnosis of IRF should be suspected in front of a patient with abdominal pain, hypertension, hydronephrosis and ESR elevation. An early diagnosis is fundamental to prevent renal failure.