Pagine elettroniche ; Caso Contributivo
Interessamento cardiaco nella sindrome di Churg-Strauss
CARDIAC INVOLVEMENT IN CHURG-STRAUSS SYNDROME
A. Amaddeo, F. Marchetti, M. Londero, M. Maschio, A. Benettoni, A. Ventura
Aprile 2011 - pagg. 259 -261
Abstract
We report the case of a 15-year-old boy with asthenia,
hypereosinophilia, a macular-papular rash in his hands
and weight loss in the previous two months. Spirometry showed
severe bronchial obstruction and transthoracic echocardiography
revealed a peri-miocardial involvement. Churg-Strauss syndrome
was diagnosed and appropriate treatment was initiated.
Cardiac involvement it is not included in the official diagnostic
criteria of CSS despite it is common (up to 60% of cases) and
represents the major cause of mortality.
Parole chiave
Classificazione MeSH
Bibliografia
1. Masi AT, Hunder GG, Lie JT et al. The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis). Arthritis Rheum 1990;33:1094-00.
2. Jennette JC, Falk RJ, Andrassy K, et al. Nomenclature of systemic vasculitides. Proposal of an international consensus conference. Arthritis Rheum 1994;37:187-92.
3. Baldini C, Talarico R, Della Rossa A. Clinical manifestations and treatment of Churg-Strauss syndrome. Rheum Dis Clin North Am 2010;36:527-43.
4. Pagnoux C, Guilpain P, Guillevin L. Churg-Strauss syndrome. Curr Opin Rheumatol 2007;19:25-32.
5. Pelà G, Tirabassi G, Pattoneri P. Cardiac involvement in the Churg-Strauss syndrome. Am J Cardiol 2006;97:1519-24.
6. Pagnoux C, Guillevin L. Churg-Strauss syndrome: evidence for disease subtypes? Curr Opin Rheumatol 2010;22:21-8.
Corrispondenza: alessandro.amaddeo@gmail.com