Pagine elettroniche ; Caso Contributivo
Un caso di emofilia acquisita
A case of acquired haemophilia
A. De Cunto, P. Pasquinelli, C. Biasioli, V. Agostini, M. Pocecco
Giugno 2011 - pagg. 397 -398
Abstract
The case of a boy who presented with an isolated gross haematuria is reported. In the previous days he referred a muscular haematoma after a minimal trauma. Coagulation studies showed a prolonged activated partial thromboplastin time (90 sec), not corrected by incubating a sample of his blood with equal volumes of normal plasma (mixing study). A factor VIII level (FVIII) less than 1% was detected and a FVIII inhibitor of 2 Bethesda unit was dosed. Steroid treatment was started with prompt resolution of “acquired haemophilia”.
Classificazione MeSH
Bibliografia
1. Franchini M, Zaffanello M, Lippi G. Acquired hemophilia in pediatrics: a systematic review. Pediatr Blood Cancer 2010;55:606-11.
2. Shetty S, Bhave M, Ghosh K. Acquired hemophilia A: diagnosis, aetiology, clinical spectrum and treatment options. Autoimmun Rev 2011;10:311-6.
Corrispondenza: angela.decunto@libero.it