Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Cuore e Turner: cosa c’θ oltre la coartazione?

Heart and Turner Syndrome: what's beyond coarctation?

E. Mascheroni, E. Berton, G. Tornese

Gennaio 2015 - pagg. 57 -58

Abstract
A young woman affected by Turner syndrome undergoes periodic cardiac monitoring. Her last ECG documented QT prolongation. QT prolongation is reported in patients with Turner syndrome. This electrophysiological abnor-mality is probably due to an intrinsic defect in the regula-tion of the cardiovascular system. Although a long QT is more likely to be found in these patients, no severe life-threatening tachyarrhythmias have been described so far. Paediatricians should reassure Turner patients about the prognosis of this electrophysiological abnormality while recommending the cardiologic follow up.
Parole chiave
IT Prolungamento del QT Sindrome di Turner
EN QT prolongation Turner syndrome
Suggerite dall'AI
IT cardiopatia cuore
Classificazione MeSH
Aortic Coarctation (20) Electrocardiography (47) Heart Defects, Congenital (64) Long QT Syndrome (26) Turner Syndrome (29)
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Bibliografia



Bibliografia
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Corrispondenza: elimascheroni@virgilio.it