Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Pagine elettroniche ; Caso Contributivo

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Edema acuto emorragico della prima infanzia
(porpora di Seidlmayer)

ACUTE HEMORRAGIC EDEMA IN YOUNG CHILDREN (SEIDLMAYER PURPURA)

Alessandro Tagliabue, Alberto Bettinelli, Felice Cogliati

SC di Pediatria, Ospedale S. Leopoldo Mandic, Merate (Lecco)

Giugno 2009 - pagg. 393 -394

Abstract
Acute hemorrhagic edema is an uncommon leukocytoclastic small-vessel vasculitis that may affect young children. In literature only few cases have been reported (294 cases). In many cases the disease developed after a simple acute infection. The exanthema includes large, round, red to purpuric plaques predominant over the cheeks, ears and extremities and often tender edema of face. Involvement of body systems is rare. The children recover spontaneously without sequelae. We report a case of a 9-month boy, who presented with cockade purpura one week after gastroenteric infection. This is the second case described in our pediatric division in 33 years.

Corrispondenza: a.bettinelli@ospedale.lecco.it