Pagine elettroniche ; Caso Contributivo
La picnocitosi infantile: una causa rara ma non infrequente di anemia emolitica neonatale severa
INFANTILE PYKNOCYTOSIS: A RARE BUT NOT INFREQUENT CAUSE OF SEVERE NEONATAL HAEMOLYTIC ANAEMIA
Anna Maria Aurino, Rosanna Di Concilio, Giovanna D’urzo, Maria Amendolara, Carmelina Romano, Giulia Attianese, Silvana Mauriello, Cecilia Di Filippo, Giovanni Amendola
Unità Operativa Complessa di Pediatria - TIN, Ospedale “Umberto I”, Nocera Inferiore, Salerno
Marzo 2011 - pagg. 191 -192
Abstract
The diagnosis and treatment of six patients with infantile
pyknocytosis are reported. The clinical course and the diagnostic
work-up are shown. All the patients necessitated therapy:
phototherapy in five patients and one red blood cell transfusion in
all of them; in two patients, because of the persistence of
haemolysis and pyknocytosis with inadequate erythropoiesis, a
brief course of erythropoietin treatment was undertaken with an
excellent response and no side effects. Infantile pyknocytosis is a
rare but not infrequent disease: physicians caring for a neonate
with haemolytic anaemia should not forget this disease in the differential
diagnosis.
Parole chiave
Suggerite dall'AI
EN
neonate
Classificazione MeSH
Bibliografia
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