Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Interessamento cardiaco nella sindrome di Churg-Strauss

CARDIAC INVOLVEMENT IN CHURG-STRAUSS SYNDROME

Alessandro Amaddeo1, Federico Marchetti1, Margherita Londero2, Massimo Maschio1, Alessandra Benettoni3, Alessandro Ventura1

1Clinica Pediatrica, IRCCS “Burlo Garofolo”, Università di Trieste
2UOC di Pediatria, PO “Sant’Antonio”, San Daniele del Friuli (Udine)
3Servizio di Cardiologia, IRCCS “Burlo Garofolo”, Università di Trieste

Aprile 2011 - pagg. 259 -261

Abstract
We report the case of a 15-year-old boy with asthenia, hypereosinophilia, a macular-papular rash in his hands and weight loss in the previous two months. Spirometry showed severe bronchial obstruction and transthoracic echocardiography revealed a peri-miocardial involvement. Churg-Strauss syndrome was diagnosed and appropriate treatment was initiated. Cardiac involvement it is not included in the official diagnostic criteria of CSS despite it is common (up to 60% of cases) and represents the major cause of mortality.
Parole chiave
Churg-Strauss syndrome Miocardial involvement
Suggerite dall'AI
cardiomiopatia eosinophilia vasculite vasculitis
Classificazione MeSH
Respiratory Tract Diseases Bronchial Diseases Bronchial Hyperreactivity (20)
Cardiovascular Diseases Vascular Diseases Vasculitis Systemic Vasculitis Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis Churg-Strauss Syndrome (3)
Hemic and Lymphatic Diseases Hematologic Diseases Leukocyte Disorders Eosinophilia (33)
Skin and Connective Tissue Diseases Skin Diseases Exanthema (68)
Cardiovascular Diseases Heart Diseases Cardiomyopathies Myocarditis (29)
Cardiovascular Diseases Heart Diseases Pericarditis (11)
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Bibliografia
1. Masi AT, Hunder GG, Lie JT et al. The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis). Arthritis Rheum 1990;33:1094-00. 2. Jennette JC, Falk RJ, Andrassy K, et al. Nomenclature of systemic vasculitides. Proposal of an international consensus conference. Arthritis Rheum 1994;37:187-92. 3. Baldini C, Talarico R, Della Rossa A. Clinical manifestations and treatment of Churg-Strauss syndrome. Rheum Dis Clin North Am 2010;36:527-43. 4. Pagnoux C, Guilpain P, Guillevin L. Churg-Strauss syndrome. Curr Opin Rheumatol 2007;19:25-32. 5. Pelà G, Tirabassi G, Pattoneri P. Cardiac involvement in the Churg-Strauss syndrome. Am J Cardiol 2006;97:1519-24. 6. Pagnoux C, Guillevin L. Churg-Strauss syndrome: evidence for disease subtypes? Curr Opin Rheumatol 2010;22:21-8.

Corrispondenza: alessandro.amaddeo@gmail.com