Pagine elettroniche
Quando la sferocitosi incontra il chirurgo
Surgical treatment of hereditary spherocytosis
Chiara Bibalo
Scuola di Specializzazione in Pediatria, IRCCS Materno-Infantile “Burlo Garofolo”, Università di Trieste
Giugno 2015 - pagg. 391 -392
Abstract
Summary Hereditary spherocytosis is a common inherited disorder
that is characterized by anaemia, jaundice and splenomegaly.
It is reported worldwide and is the most common inherited
anaemia in individuals of northern European ancestry. Clinical
severity is variable with most of patients having a wellcompensated
haemolytic anaemia. Some individuals are
asymptomatic, whereas others have severe haemolytic anaemia
requiring erythrocyte transfusion. Common complications
are cholelithiasis and aplastic crises. Splenectomy is curative
and it is indicated in children with moderately-severe and severe
hereditary spherocytosis and in patients with symptoms of
cholelithiasis.
Classificazione MeSH
Contenuto riservato
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Corrispondenza: chiara.bibalo@gmail.com
