Aggiornamento
Corea reumatica: tre “C” che dicono tutto
Three Cs that say everything about rheumatic chorea
Francesco Baldo1, Andrea Taddio1,2, Alessandro Ventura1
1Universitŕ di Trieste
2IRCCS Materno-Infantile “Burlo Garofolo”, Trieste
Maggio 2018 - pagg. 295 -300
Abstract
Although Sydenham’s chorea is an uncommon manifestation of rheumatic fever, it is still
the most frequent cause of chorea in children. It is characterized by the sudden appearance
of involuntary and disturbing movements of the upper and lower body, associated
with grimaces, dysarthria and various psychiatric features. The paper describes two cases
of Sydenham’s chorea to portray the clinical heterogeneity of the disease, its association
with heart involvement and the efficacy of corticosteroids both in resolving the
symptoms and in preventing the relapses, at least when administered in the early stage
of the disease. After an introductive description of the disease itself, its epidemiology
and clinical features, with reference to our thirty-year experience at Burlo Garofolo, Trieste,
is described. The paper also highlights the peculiar traits that paediatricians must remember
in order to correctly identify it, especially its close relationship with rheumatic
carditis, and the tricks to differentiate it from other conditions that may present with choreic
movements. The article also analyses the current treatments available, especially the
use of corticosteroids, which has been routinely employed to treat patients, and reports
the main positive outcomes.
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Corrispondenza: francescobaldo11@yahoo.it