Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
Login Abbonamenti Pubblicazioni Carrello Registrazione Perché registrarsi? Contatti

Aggiornamento monografico

PDF

Sindrome del bambino plasmato e displasia dell’anca

MOULDED BABY SYNDROME AND CONGENITAL DYSPLASIA OF THE HIP

1RAFFAELE SCAPINELLI, 2ANNA CAROLA SCAPINELLI

1Istituto di Clinica Ortopedica, Università degli Studi di Padova
2Istituto di Clinica Ginecologica e Ostetrica, Università di Sassari

Marzo 1997 - pagg. 153 -157

Abstract
Congenital postural deformities, collectively referred to as moulded baby syndrome to underline the importance of intrauterine “moulding” in their origin, mainly include plagiocephaly, torticollis, scoliosis, pelvic obliquity, torsional abnormalities of the femura and tibiae, genu recurvatum and foot deformities. In the first 6 to 7 months after birth these newborn infants have a strong tendency to assume a lateral oblique lie, which worsen some of the neonatal deformities. The adducted hip, i.e. the hip opposite to the decubitus, usually shows limitation of abduction and must be considered at risk for mechanical inhibition of osteochondral growth and plastic deformation of the articular soft tissues. These changes are promptly reversible when posture is corrected. In a number of cases, evolution towards dysplastic- like changes can be expected, radiologically indistinguishable from CDH (Congenital Dysplasia of the Hip) of common type. The Ortolani’s maneuvre is usually negative and this explains the late or missed diagnoses. In the Author’s series of 187 moulded babies, 44,6% showed on ultrasound and X-ray examination a delayed development (hypoplasia) of the adducted hip and 10,2% definite dysplastic changes. The lateral oblique lie should therefore be considered among the signs suggesting CDH.
Parole chiave
Congenital dislocation of the hip Congenital pelvic obliquity Congenital postural deformities Displasia congenita dell'anca Moulded baby syndrome Obliquità pelvica congenita Sindrome del neonato modellato
Classificazione MeSH
Congenital, Hereditary, and Neonatal Diseases and Abnormalities Congenital Abnormalities Musculoskeletal Abnormalities Developmental Dysplasia of the Hip Hip Dislocation, Congenital (15)
Congenital, Hereditary, and Neonatal Diseases and Abnormalities Congenital Abnormalities Musculoskeletal Abnormalities (4)
Congenital, Hereditary, and Neonatal Diseases and Abnormalities Congenital Abnormalities Musculoskeletal Abnormalities Craniofacial Abnormalities Plagiocephaly (5)
Musculoskeletal and Neural Physiological Phenomena Musculoskeletal Physiological Phenomena Posture (11)
Musculoskeletal Diseases Bone Diseases Spinal Diseases Spinal Curvatures Scoliosis (33)
Pathological Conditions, Signs and Symptoms Signs and Symptoms Neurologic Manifestations Dyskinesias Dystonia Torticollis (19)
Diagnosis Diagnostic Techniques and Procedures Diagnostic Imaging Ultrasonography (138)
Leggi anche
RI Domande e risposte
Petto carenato Scoliosi: ginnastica posturale e attività sportiva Screening e celiachia
· 2024
Musculoskeletal Abnormalities/Pectus Carinatum, Posture, Scoliosis
RI Se la conosci la riconosci
La sindrome di Poland
Abramo M, Selicorni A. · 2024
Musculoskeletal Abnormalities, Plagiocephaly/Musculoskeletal Abnormalities, Hip Dislocation, Congenital/Musculoskeletal Abnormalities
RI Aggiornamento
Torcicollo in età pediatrica: come orientarsi per non sbagliare
Cruciani C, Borelli AI, Palluzzi F, Bonvicini F, · 2025
Torticollis, Scoliosis
RI Il graffio
L’Europa al tempo del coronavirus
· 2020
Musculoskeletal Abnormalities/Developmental Dysplasia of the Hip, Hip Dislocation, Congenital, Ultrasonography
RI Lettere
Screening ecografico della lussazione congenita dell’anca? Farsi bambino, in modo “consapevole e re...
· 2020
Musculoskeletal Abnormalities/Hip Dislocation, Congenital, Hip Dislocation, Congenital, Ultrasonography
Leggi il PDF completo »
Bibliografia
gnificance of retention of foetal position of the limbs. Proceedings Amer Acad Orthop Surgeons. J Bone Jt Surg 35-A, 498, 1953.
2. Bauer F: Die Entstehung der angeborenen Hüftverrenkung durch Zwangshaltung. Z Orthop 65, 318-40, 1936.
3. Browne D: Congenital deformities of mechanical origin. Arch Dis Child 30, 37-41, 1955.
4. Dunn PM: Congenital postural deformities. Brit Med Bull 32, 71-76, 1976.
5. Gladel W: Die Schrägseitenlage des Säuglings als gemeinensame Ursache der Säuglingsskoliose und Huftluxation. Mschr Kinderheilkunde 117, 196-198, 1969.
6. Lloyd-Roberts GC, Pilcher MF: Structural idiopathic scoliosis in infancy: a study of the natural history of 100 patients. J Bone Jt Surg 47-B, 520-523, 1965.
7. Mau H: Zur Ätiopathogenese von skoliose, Hüftdysplasie und Schiefhals im Säuglinssalter. Z Orthop 117, 784-789, 1979.
8. Mau H: The “seven sign syndrome” and infantile scoliosis. La Clinica Ortopedica, Int J Orthop Surg Traum, Special Issue, 125-134, 1991.
9. Ortolani M, Ortolani M Sr: Displasia delle anche e posture pre e post-natali. La Clinica Ortopedica 26, 219-233, 1975-76.
10. Palmén K: Prevention of congenital dislocation of the hip. Acta Orthop Scand 55, Suppl. 208, 1984.
11. Rauterberg E, Tönnis D: Untersuchungen über der Entstehung und den Verlauf der Säuglingsskoliose. Z Orthop 109, 676-689, 1971.
12. Scapinelli R, Ortolani M, Ferraro C: Posture postnatali e ritardato sviluppo unilaterale dell’anca (ipoplasia posturale). Annali della Società di Ortopedia e Traumatologia dell’Italia Centrale (SOTIC), Aulo Gaggi Ed., Bologna, 3, 113-118, 1985.
13. Scapinelli R: Pseudodisplasie ed ipoplasie delle anche nel primo anno di vita. La Clinica Ortopedica, Int J Orthop Surg Traum 27, 51- 80, 1988.
14. Scapinelli R: L’anca addotta nel neonato con obliquità pelvica congenita: un’anca a rischio. La Clinica Ortopedica, Int J Orthop Surg Traum, Special Issue, 143-157 1991.
15. Scapinelli R: Developmental dysplasia of the adducted hip in the moulded baby syndrome. EFORT Proceedings. J Bone Jt Surg 75-B, Suppl. II, 159, 1993.
16. Weissman SL: Congenital pelvic obliquity. Clin Orthop 36, 118-127, 1964.
17. Wilkinson JA: Congenital displacement of the hip joint. Springer-Verlag, Berlin, Heidelberg, New York, Tokio, 1985.
18. Zanardo V, Scapinelli AC: Le deformità del capo nel neonato a termine e pretermine. La Clinica Ortopedica, Int J Orthop Surg Traum, Special Issue, 53-56, 1991.