Aggiornamento monografico
Emangiomi e malformazioni vascolari
HEMANGIOMAS AND VASCULAR MALFORMATIONS
PIETRO DALMONTE, GIANLAURO BAVA, NINO CAMASSA, LUCIO ZANNINI
Divisione di Cardiochirurgia e Chirurgia Vascolare, Istituto G. Gaslini, Genova
Maggio 1997 - pagg. 293 -300
Abstract
Congenital vascular malformations represent
a heterogeneous group of isolated or
multiple abnormalities, sometimes associated
with complex congenital syndromes.
They rarely occur in the daily practice of
vascular surgeons, are often misdiagnosed
and, for the most part, left untreated.
The current classification recognizes two distinct
groups of lesions, hemangiomas and
vascular malformations. Hemangiomas are
not present at birth, proliferate in the first
year of life and then involute with complete
resolution in over 50% of children by the
6th-8th year of life; a therapeutic intervention
(mainly corticosteroids or interferon-alfa
2a) is required only for life-threatening
hemangiomas.
Vascular malformations are always present
at birth, grow along with the child, and never
involute. Surgery and/or sclerotherapy
are indicated for low-flow malformations
(venous and/or lymphatic forms), whereas
embolization followed by surgery is the first-
choice procedure for arteriovenous
malformations. Laser therapy is ideal for
cutaneous capillary malformations (portwine
stains). Knowledege of classification and
evolution of congenital vascular lesions is
essential for planning the most appropriate
treatment.
Parole chiave
Suggerite dall'AI
Classificazione MeSH
Bibliografia
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8. Samuel M, Spitz L: Klippel-Trenaunay syndrome: clinical features, complications and management in children. Br J Surg Jun 82(6), 757-61, 1995.
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2. Lemarchand-Venencie F: Management of Hemangioma in the infant. J Mal Vasc 17(1), 33-40, 1992.
3. Ezekowitz RA, Mulliken JB, Folkman J: Interferon alfa-2a therapy for life-threatening hemangiomas of infancy. N Engl J Med May 28, 326(22), 1456-1463, 1992.
4. Enjolras O, Mulliken JB: The current management of vascular birthmarks. Pediatr Dermatol Dec 10(4), 311-313, 1993.
5. Alvarez-Franco M, Paller AS: What syndrome is this? Congenital Kasabach-Merritt syndrome. Pediatr Dermatol Mar 11(1), 79-81, 1994.
6. de Lorimier AA: Sclerotherapy for venous malformation. J Pediatr Surg Feb 30(2), 188- 93, 1995.
7. Bartels C, Horsch S: Classification of congenital arterial and venous vascular malformations. Angiology Mar 46(3), 191-200, 1995.
8. Samuel M, Spitz L: Klippel-Trenaunay syndrome: clinical features, complications and management in children. Br J Surg Jun 82(6), 757-61, 1995.
9. Waner M, Suen JY: Management of congenital vascular lesions of the head and the neck. Oncology Oct 9(10), 989-997, 1995.
