Caso contributivo
Due rari casi di iperlipasemia pancreatica benigna in età pediatrica
Two rare cases of benign pancreatic hyperlipasemia in children
Marta Cofini1, Francesco Quadrozzi2
1Clinica Pediatrica, Università di Perugia
2Clinica Chirurgica, Università di L’Aquila
Maggio 2015
Abstract
Benign pancreatic hyperenzimemia is a newly identified condition, characterized by a chronic elevation, with swinging-rate of pancreatic amylase and/or lipase in absence of pancreatic disease. The paper describes two rare cases of pancreatic benign hyperlipasemia in children (to date only two case reports are described in the literature). Knowing this condition could be very useful to paediatricians, gastroenterologists and surgeons in the diagnosis and management of this syndrome. Pancreatic benign hyperlipasemia remains a diagnosis of exclusion, after having performed all the diagnostic investigations for acute, chronic or neoplastic pancreatic pathology.
Contenuto riservato
Per leggere l'articolo è necessario effettuare il login.
Parole chiave
Bibliografia
Bibliografia
- Cofini M, Favorite P, Quadrozzi F. Pancreatite acuta in età pediatrica: nostra esperienza su 52 casi. Minerva Pediatr 2014;66:275-80.
- Depsames R, Fireman Z, Niv E, Kopelman Y. Macroamylasemia as the first manifestation of celiac disease. Case Rep Gastroenterol 2008;2(2):196-8.
- Rabsztyn A, Green PH, Berti I, Fasano A, Perman JA, Horvath K. Macroamylasemia in patients with celiac disease. Am J Gastroenterol 2001;96:1096-100.
- Gullo L, Laghi L, Migliori M, et al. PINK1 and PRSS1 mutations in benign pancreatic hyperenzymemia. Pancreas 2008;37(1):31-5.
- Gullo L, Migliori M, Fusaroli P, Caletti G. Familial association of benign pancreatic hyperenzymemia and pancreatic cancer. Gut 2007;56(9):1323-4.
- Lionetti E, Francavilla R, Leonardi S, et al. Two rare cases of benign hyperlipasemia in children. World J Clin Cases 2014;2(1):16-9.
- Gullo L, Lucrezio L, Calculli L, et al. Magnetic resonance cholangiopancreatography in asymptomatic pancreatic hyperenzymemia. Pancreas 2009;38(4):396-400.
- Pezzilli R, Morselli-Labate AM, Casadei R, et al. Chronic asymptomatic pancreatic hyperenzymemia is a benign condition in only half of the cases: a prospective study. Scand J Gastroenterol 2009;44:888-93.
- Testoni PA, Mariani A, Curioni S, Giussani A, Masci E. Pancreatic ductal abnormalities documented by secretin-enhanced MRCP in asymptomatic subjects with chronic pancreatic hyperenzymemia. Am J Gastroenterol 2009;69:1251-61.
- Catalano MF, Sahai A, Levy M, et al. EUS-based criteria for the diagnosis of chronic pancreatitis. Gastrointest Endosc 2009;69:1251-61.
