Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Un lobo polmonare iperlucente

Unilateral hyperlucent lung in childhood

Giuseppe Vieni1, Sara Pusceddu1, Lorenzo Mambelli1, Fabrizio Pugliese1, Venerino Poletti2,Federico Marchetti1
1UOC di Pediatria e Neonatologia, Ospedale di Ravenna, AUSL della Romagna
2Dipartimento Toracico, Ospedale G.B. Morgagni, Forlė
and Department of Respiratory Diseases & Allergology, Aarhus University Hospital, Aarhus (DK)

Novembre 2015

Abstract
The paper describes the case of a 7-year-old female child with a history of chronic cough following an acute respiratory infection and unilateral hyperlucent lung on chest radiograph. The diagnosis was Swyer-James-MacLeod syndrome, based on characteristic findings on chest TC. Swyer-James-MacLeod syndrome is a post-infectious form of bronchiolitis obliterans that damages the lung during early childhood. Affected patients frequently have a history of recurrent pulmonary infection and present with nonspecific respiratory symptoms. The diagnosis is made with characteristic radiographic findings such as asymmetric hyperlucency of the lung or lobe, reduction of parenchimal vascularity and air-trapping of the affected parenchyma. The differential diagnosis often requires bronchoscopy and angio-TC or lung scintigraphy is necessary in some cases. The therapy is based on management of lung infections and bronchial obstruction. The prognosis is generally good.
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Parole chiave
Lobo polmonare iperlucente Sindrome di Swyer-James-MacLeod
Suggerite dall'AI
Bronchiolite obliterante Swyer-James-MacLeod syndrome
Bibliografia
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