Caso contributivo
Quale linfonodo sei? La malattia di Rosai-Dorfman in un adolescente
Rosai-Dorfman disease in an adolescent
Caterina Radice1, Gloria Marescotti2, Martina Serafini2, Giuliana Turlà1, Maria Teresa Minguzzi3, Francesco Soprani4, Federico Marchetti1
1UOC di Pediatria e Neonatologia, Ospedale di Ravenna, AUSL della Romagna
2Scuola di Specializzazione in Pediatria, Universitaria di Ferrara
3UOC di Radiodiagnostica, 4UOC di Otorinolaringoiatria, Ospedale di Ravenna, AUSL della Romagna
Maggio 2019
Abstract
The paper reports the case of a 13-year-old adolescent presenting with a right-sided submandibular lymph node swelling in absence of any other systemic symptoms. The histological exam documented Rosai-Dorfman disease (RD). The MRI of the head reported an infiltrative lesion of the nasal choanae that was confirmed by PET/CT and radically excised. In about 10% of cases RD may involve nasal choanae and can be asymptomatic or present with obstructions, epistasis, deformity in the nasal dorsum and hyposmia. By considering a recent international Consensus, the pa-per discusses the diagnostic and therapeutic approach to the localised forms of the Rosai-Dorfman disease.
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