Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Hydroxyurea

11 articoli — 2004-2025

RI Protocolli di diagnosi e terapia
Facciamo il punto sull’anemia falciforme

Tessitore A, Cuzzubbo D, Russo G.

2025/5 — pag. 296-298 — DOI

Sickle cell disease (SCD) is an increasingly relevant condition in Italy due to rising immigration from high-prevalence regions. Early diagnosis through newborn screening and comprehensive management - including hydroxyurea, antibiotic prophylaxis, t...

EL I Poster degli specializzandi
Accesso libero
Drepanocitosi e osteonecrosi avascolare della testa del femore

Perfetto F, Pasquali E, Biserna L, Iacono A, Farneti C, Radice C, Marchetti F

2025/5 — pag. 123-124 — DOI

A 10.5-year-old girl with homozygous sickle cell disease on chronic treatment with hydroxyurea, blood transfusions and erythroexchange presented with sudden right thigh pain and limping, without trauma or fever. Imaging and lab results indicated avas...

RI Pagine elettroniche
Lesioni ossee simmetriche e drepanocitosi

Franzone D, Chianucci B, Basso L, Guardo D, Bellini T, Piccotti E.

2023/6 — pag. 399-402 — DOI

An 8-year-old boy suffering from sickle cell disease (SCD) was admitted to emergency unit complaining of moderate-to-severe pain in his lower limbs. He received chronic transfusion therapy and hydroxyurea. Apparently, he had never experienced vaso-oc...

EL Pediatria per immagini
Lesioni ossee simmetriche e drepanocitosi

Franzone D, Chianucci B, Basso L, Guardo D, Bellini T, Piccotti E

2023/6 — pag. 100-101 — DOI

An 8-year-old boy suffering from sickle cell disease (SCD) was admitted to emergency unit complaining of moderate-to-severe pain in his lower limbs. He received chronic transfusion therapy and hydroxyurea. Apparently, he had never experienced vaso-oc...

RI Pagine elettroniche
Anemia falciforme e sindrome toracica acuta

G. Graziani, J. Gencarelli, C. Lama, S. Brocchi, L. Biserna, C. Radice, F. Marchetti

2020/6 — pag. 392-394

EL Protocolli di diagnosi e terapia
Anemia falciforme e sindrome toracica acuta

G. Graziani, J. Gencarelli, C. Lama, S. Brocchi, L. Biserna, C. Radice, F. Marchetti

2020/6 — pag. 126-129 — DOI

RI Aggiornamento
La gestione condivisa ospedale-territorio del bambino con malattia drepanocitica

P. Samperi, R. Colombatti, E. Cannata, L. Sainati, G. Russo

2017/10 — pag. 629-635

Sickle cell disease is a hereditary autosomal disease of haemoglobin characterized by chronic haemolytic anaemia, vaso-occlusive painful crisis, organ damage and increased susceptibility to infections. In recent years, the number of patients with s...

RI Aggiornamento monografico
L'anemia falciforme

M. Lazzerini, M. Rabusin

2006/4 — pag. 223-234

Sickle cell disease (SCD) is one of the most prevalent haemoglobinopathies in the world, being related to areas where malaria is or was endemic. In Italy the majority of patients still live in Sicily, where the overall HbS gene frequency is 2%. Domes...

EL Caso Clinico Interattivo
Accesso libero
Una dattilite bilaterale simmetrica

M. Lazzerini

2004/2