Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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splenectomia

11 articoli — 2000-2024

RI Pagine elettroniche
Sferocitosi: una famiglia... tre malattie!

Ferrara D, Giordano C, Borsellino Z, Cuccia L, Ruffo GB, Corsello G.

2024/1 — pag. 54-57 — DOI

The paper describes the cases of three siblings affected by Hereditary Spherocytosis (HS). The different clinical presentations in the same family are examples of the heterogeneity of this pathology. HS is a common inherited type of haemolytic anaemi...

EL I Poster degli specializzandi
Accesso libero
Quando pensare alla splenectomia in presenza di Beta-talassemia con drepanocitosi?

Stera G, Legnani E, Grasso A

2024/1 — pag. 21-21 — DOI

The authors describe the positive effect of splenectomy in two brothers affected by micro-drepanocytosis....

EL Caso contributivo
Un’emolisi ben mascherata

G. Del Borrello

2018/6

Chronic haemolytic anaemia is a pathophysiological process that can be the expression of many possible etiologies (e.g. a congenital defect of a membrane protein, immune-mediated destruction, enzymopathies, altered erythrocyte development). The paper...

RI Pagine elettroniche
Quando la sferocitosi incontra il chirurgo

C. Bibalo

2015/6 — pag. 391-392

Summary Hereditary spherocytosis is a common inherited disorder that is characterized by anaemia, jaundice and splenomegaly. It is reported worldwide and is the most common inherited anaemia in individuals of northern European ancestry. Clinical ...

EL Caso contributivo
Quando la sferocitosi incontra il chirurgo

C. Bibalo

2015/6

Summary Hereditary spherocytosis is a common inherited disorder that is characterized by anaemia, jaundice and splenomegaly. It is reported worldwide and is the most common inherited anaemia in individuals of northern European ancestry. Clinical ...

RI Rubrica iconografica
Wandering spleen in età pediatrica

L. Radillo, M. Maschio, A. Taddio, S. Furlan, E. Barbi

2014/10 — pag. 659-662

RI Articolo speciale
Accesso libero
Cinquant’anni di talassemia, a Ferrara

F. Panizon

2011/10 — pag. 644-645

EL Contributi Originali - Casi contributivi
Accesso libero
PIastrinopenia isolata x-linked da mutazione missense del gene Wasp: descrizione di un caso

C Locatelli, C Malaventura, R Ciambra, M Pocecco, L. D Notarangelo, L. D Notarangelo

2004/7

EL Contributi Originali - Casi contributivi
Accesso libero
Piastrinopenia cronica multiresistente in bambina con sindrome linfoproliferativa autoimmune (ALPS). Efficacia della ciclofosfamide

E. Barth, M. Rabusin G.A. Zanazzo, P. Tamaro

2001/8

RI Problemi non correnti
Accesso libero
Indicazioni alla splenectomia

P. Tamaro, E. Barth

2000/6 — pag. 373-375

Progress in surgical techniques and in management and understanding of haematologic diseases stimulate a critical reappraisal of splenectomy. Spleen plays an important role in removing normal and abnormal cells from the blood and in providing immun...