Problemi speciali
Algodistrofia: cosa deve sapere il pediatra
Complex regional pain syndrome (CRPS) and children: what paediatricians should know
Giovanna Ferrara1, Giada Zanella1, Giulia Gortani2, Irene Bruno2, Serena Pastore2, Marco Carbone2, Andrea Taddio1,2, Alessandro Ventura1,2
1Università di Trieste; 2IRCCS Materno-Infantile “Burlo Garofolo”, Trieste
Aprile 2017 - pagg. 237 -242
Abstract
Complex regional pain syndrome (CRPS) is a debilitating pain condition characterized
by continuous and severe pain that usually affects a limb. The syndrome is well-described
in adults, but can also affect children and adolescents. Symptoms include disproportionate
pain, allodynia and hyperalgesia; clinical signs are swelling or oedema, changes
in skin’s colour, temperature and tropism, hyperhidrosis and motor disturbances of
the affected limb. The exact pathogenesis of CRPS is unknown, although several different
mechanisms have been suggested. The diagnosis is clinical: the adult criteria for
CRPS and imaging showing localized osteoporosis can be useful. Treatment of CRPS in
children consists of a multidisciplinary approach combining physical, psychological and
pharmacological therapies: the main goal is early mobilization of the affected limb through
intensive physiotherapy. Drugs reducing physical and neuropathic pain may be
helpful to perform the exercises; also patients’ families and cognitive-behavioural support
can play an important role in the remission of the syndrome. The prognosis in paediatric
CRPS is favourable, however relapses are common.
Classificazione MeSH
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Corrispondenza: giovanna.ferrara@gmail.com