Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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Problemi speciali

L’idrosadenite suppurativa nella popolazione pediatrica

Hidradenitis suppurativa in paediatric population

Benedetta Bossini1, Michele Mazzolai1, Alberto Tommasini2, Sergio Crovella2, Irene Berti2, Egidio Barbi1,2

1Dipartimento di Scienze Mediche, Chirurgiche e della Salute, Università di Trieste
2IRCCS Materno-Infantile “Burlo Garofolo”, Trieste

Gennaio 2019 - pagg. 28 -32

Abstract
Hidradenitis suppurativa (HS) is a chronic and recurrent skin disease affecting apocrine gland-bearing regions. Typical lesions are nodules and abscesses that result in sinus tracts, fistulas and eventually scarring. Prepubertal onset of HS is quite rare, representing only 2% of all HS cases, which are frequently expression of genetic forms, hormonal imbalances or systemic autoinflammatory diseases. Therapy is severity-tailored ranging from topical antibiotics to monoclonal antibodies, saving surgery for unresponsive cases. Early diagnosis and prompt treatment are fundamental to arrest disease progression to milder stages, giving children the opportunity to keep a good quality of life without getting stuck on this condition.
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Bibliografia
1. Saunte DML, Jemec GBE. Hidradenitis suppurativa: advances in diagnosis and treatment. JAMA 2017; 318(20): 2019-32. 2. Liy-Wong C, Pope E, Lara-Corrales I. Hidradenitis suppurativa in the pediatric population. J Am Acad Dermatol 2015;73(5 Suppl 1):S36-41. 3. Vekic DA, Frew J, Cains GD. Hidradenitis suppurativa, a review of pathogenesis, associations and management. Part 1. Australas J Dermatol 2018;59(4):267-77. 4. Napolitano M, Megna M, Timoshchuk EA, et al. Hidradenitis suppurativa: from pathogenesis to diagnosis and treatment. Clin Cosmet Investig Dermatol 2017;10:105- 15. 5. Braunberger TL, Nicholson CL, Gold L, et al. Hidradenitis suppurativa in children: The Henry Ford Experience. Pediatr Dermatol 2018;35(3):370-3. 6. Mikkelsen PR, Jemec GB. Hidradenitis suppurativa in children and adolescents: a review of treatments options. Paediatr Drugs 2014;16(6):483-9. 7. Scheinfeld N. Hidradenitis suppurativa in prepubescent and pubescent children. Clin Dermatol 2015;33(3):316-9. 8. Vekic DA, Cains GD. Hidradenitis suppurativa, a review of pathogenesis, associations and management. Part 2. Australas J Dermatol 2018;59(4):261-6. 9. Vekic DA. Hidradenitis suppurativa - Management comorbities and monitoring. The Royal Australian College of Practitioner, 2017. 10. Randhawa HK, Hamilton J, Pope E. Finasteride for the treatment of hidradenitis suppurativa in children and adolescentes. JAMA Dermatol 2013;149(6):732-5. 11. Mota F, Machado S, Selores M. Hidradenitis suppurativa in children treated with finasteride: a case series. Pediatr Dermatol 2017; 34(5):578-583. 12. Palmer RA, Keefe M. Early-onset hidradenitis suppurativa. Clin Exp Dermatol 2001; 26(6):501-3.

Corrispondenza: michele.mazzolai90@gmail.com