Caso contributivo
Occhio all’asimmetria toracica alla nascita... e se fosse la sindrome di Poland?
Poland syndrome from the first day of life
Antonella Di Caprio1, Luca Bedetti2,3, Simona F. Madeo4, Laura Lucaccioni4, Federica Roversi3, Lorenzo Iughetti1,4, Alberto Berardi3
1Scuola di Specializzazione in Pediatria, 2PhD Program in Clinical and Experimental Medicine, Università di Modena e Reggio Emilia, Modena
3UO di Terapia Intensiva Neonatale, 4UO di Pediatria, AOU Policlinico di Modena
Giugno 2021 | DOI: 10.53126/MEBXXIV166
Abstract
Poland syndrome is a rare congenital disorder characterized by agenesis of the pectoralis major muscle. It is usually unilateral and right-sided and can be associated with several thoracic and upper limb defects. Early diagnosis and timely therapeutic approaches play an important role, improving the quality of life of patients and their families. This case report aims to show the benefits of early diagnosis, especially for follow-up management.
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