Aggiornamento
La gestione condivisa ospedale-territorio del bambino con malattia drepanocitica
Comprehensive management of children with sickle cell disease
Piera Samperi1, Raffaella Colombatti2, Emanuela Cannata1, Laura Sainati2, Giovanna Russo1
1Ematologia e Oncologia Pediatrica, AOU “Policlinico - Vittorio Emanuele”, Università di Catania
2Centro di Riferimento della Regione Veneto nella Diagnosi, Cura e Trattamento della Malattia Drepanocitica in Età Pediatrica, Clinica di Oncoematologia Pediatrica, AOU di Padova
Dicembre 2017 - pagg. 629 -635
Abstract
Sickle cell disease is a hereditary autosomal disease of haemoglobin characterized by
chronic haemolytic anaemia, vaso-occlusive painful crisis, organ damage and increased
susceptibility to infections. In recent years, the number of patients with sickle cell disease
increased in Italy. The paper presents an overview of the disorder, its main clinical complications,
and a review of the general management of the patient according to the international
and national guidelines.
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Corrispondenza: diberuss@unict.it
