Rivista di formazione e aggiornamento professionale del pediatra e del medico di base, fondata nel 1982. In collaborazione con l'Associazione Culturale Pediatri.
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La gestione condivisa ospedale-territorio del bambino con malattia drepanocitica

Comprehensive management of children with sickle cell disease

Piera Samperi1, Raffaella Colombatti2, Emanuela Cannata1, Laura Sainati2, Giovanna Russo1

1Ematologia e Oncologia Pediatrica, AOU “Policlinico - Vittorio Emanuele”, Università di Catania
2Centro di Riferimento della Regione Veneto nella Diagnosi, Cura e Trattamento della Malattia Drepanocitica in Età Pediatrica, Clinica di Oncoematologia Pediatrica, AOU di Padova

Dicembre 2017 - pagg. 629 -635

Abstract
Sickle cell disease is a hereditary autosomal disease of haemoglobin characterized by chronic haemolytic anaemia, vaso-occlusive painful crisis, organ damage and increased susceptibility to infections. In recent years, the number of patients with sickle cell disease increased in Italy. The paper presents an overview of the disorder, its main clinical complications, and a review of the general management of the patient according to the international and national guidelines.
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Corrispondenza: diberuss@unict.it